X-linked Hyper IgM Syndrome is a genetic disorder that is inherited in an X-linked recessive manner.What are the Causes of X-Linked Hyper IgM Syndrome? (Etiology) It is always important to discuss the effect of risk factors with your healthcare provider. Some risk factors are more important than others.Īlso, not having a risk factor does not mean that an individual will not get the condition.
A risk factor increases ones chances of getting a condition compared to an individual without the risk factors. It is important to note that having a risk factor does not mean that one will get the condition. A positive family history of X-linked Hyper IgM Syndrome is the only known risk factor for the condition.What are the Risk Factors for X-Linked Hyper IgM Syndrome? (Predisposing factors) There is no particular racial or ethnic preference observed and the condition is seen worldwide.The prevalence rate of the condition is 1 in 500,000 among the general population.This condition almost exclusively affects males X-linked Hyper IgM Syndrome is a rare, congenital condition that manifests at birth.Who gets X-Linked Hyper IgM Syndrome? (Age and Sex Distribution) A majority of individuals do not survive past early adulthood Despite continuous support and therapy, the prognosis of X-linked Hyper IgM Syndrome is poor.The management of X-linked Hyper IgM Syndrome may involve immunoglobulin therapy, bone marrow and stem cell transplants, administration of antimicrobial drugs, and dietary control.X-linked Hyper IgM Syndrome is a lethal condition if prompt and continuous medical support and treatment is not provided Due to the chronicity of the infections, children are prone to severe malnutrition and longstanding gastrointestinal disorders.Boys are frequently prone to ear infection (otitis), lung infection (pneumonia), sinusitis, and many other diseases This congenital disorder is inherited as an X-linked recessive trait and affects only males (almost all cases).Hence, the affected individuals remain immunocompromised and are unable to prevent or fight any infections that attack them X-linked Hyper IgM Syndrome is marked by reduced levels of antibodies, which is very important to a strong and robust immunity.The body is, hence, susceptible to many infections and diseases X-linked Hyper IgM Syndrome is an infrequent genetic disorder that disrupts the immune system, weakening the body immunity.What is X-Linked Hyper IgM Syndrome? (Definition/Background Information) Immunodeficiency with Hyper-IgM, Type 1.What are the other Names for this Condition? (Also known as/Synonyms)
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